The mitochondrial complex I activity is reduced in cells with impaired cystic fibrosis transmembrane conductance regulator (CFTR) function
Abstract: Cystic fibrosis (CF) is a frequent and lethal autosomal recessive disease. It results from different possible mutations in the CFTR gene, which encodes the CFTR chloride channel. We have previously studied the differential expression of genes in CF and CF corrected cell lines, and found a...
Guardado en:
| Autores principales: | Valdivieso, Ángel Gabriel, Clauzure, Mariángeles, Martín, María C., Taminelli, Guillermo, Massip Copiz, María Macarena, Sánchez, Francisco, Schulman, Gustavo, Teiber, María Luz, Santa Coloma, Tomás Antonio |
|---|---|
| Formato: | Artículo |
| Lenguaje: | Inglés |
| Publicado: |
Dominik Hartl, University of Tübingen, Germany
2019
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| Materias: | |
| Acceso en línea: | https://repositorio.uca.edu.ar/handle/123456789/8683 |
| Aporte de: |
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