The mitochondrial complex I activity is reduced in cells with impaired cystic fibrosis transmembrane conductance regulator (CFTR) function

Abstract: Cystic fibrosis (CF) is a frequent and lethal autosomal recessive disease. It results from different possible mutations in the CFTR gene, which encodes the CFTR chloride channel. We have previously studied the differential expression of genes in CF and CF corrected cell lines, and found a...

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Autores principales: Valdivieso, Ángel Gabriel, Clauzure, Mariángeles, Martín, María C., Taminelli, Guillermo, Massip Copiz, María Macarena, Sánchez, Francisco, Schulman, Gustavo, Teiber, María Luz, Santa Coloma, Tomás Antonio
Formato: Artículo
Lenguaje:Inglés
Publicado: Dominik Hartl, University of Tübingen, Germany 2019
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Acceso en línea:https://repositorio.uca.edu.ar/handle/123456789/8683
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