Primary endometriosis of umbilical location

Abstract:  Endometriosis is defined as the presence of functioning endometrial tissue outside the uterine cavity, usually within the pelvis. Exceptionally, secondary extrapelvic involvement is seen involving the skin, related to scars from previous surgeries in patients with a proven p...

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Autores principales: Franco , GF, Medina, A, Briancon Ayo , M, Moya , M, Kasparian , A
Formato: Artículo revista
Publicado: Universidad Nacional Córdoba. Facultad de Ciencias Médicas. Secretaria de Ciencia y Tecnología 2021
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Acceso en línea:https://revistas.unc.edu.ar/index.php/med/article/view/34898
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id I10-R327-article-34898
record_format ojs
institution Universidad Nacional de Córdoba
institution_str I-10
repository_str R-327
container_title_str Revista de la Facultad de Ciencias Médicas de Córdoba
format Artículo revista
topic surgery
Endometriosis
clasificacation
diagnosis
clasificación
diagnóstico
cirugía
Endometriosis
.
spellingShingle surgery
Endometriosis
clasificacation
diagnosis
clasificación
diagnóstico
cirugía
Endometriosis
.
Franco , GF
Medina, A
Briancon Ayo , M
Moya , M
Kasparian , A
Primary endometriosis of umbilical location
topic_facet surgery
Endometriosis
clasificacation
diagnosis
clasificación
diagnóstico
cirugía
Endometriosis
.
author Franco , GF
Medina, A
Briancon Ayo , M
Moya , M
Kasparian , A
author_facet Franco , GF
Medina, A
Briancon Ayo , M
Moya , M
Kasparian , A
author_sort Franco , GF
title Primary endometriosis of umbilical location
title_short Primary endometriosis of umbilical location
title_full Primary endometriosis of umbilical location
title_fullStr Primary endometriosis of umbilical location
title_full_unstemmed Primary endometriosis of umbilical location
title_sort primary endometriosis of umbilical location
description Abstract:  Endometriosis is defined as the presence of functioning endometrial tissue outside the uterine cavity, usually within the pelvis. Exceptionally, secondary extrapelvic involvement is seen involving the skin, related to scars from previous surgeries in patients with a proven pelvic endometriosis. Primary extrapelvic endometriosis (without pelvic involvement) is exceptional and its prevalence is unknown. There are just a few case reports of perianal, inguinal or other regions involvement. The age of presentation of extrapelvic cases ranges between 30 and 40 years, in contrast to cases with pelvic involvement, between 25 and 30 years. We present a 35-year-old woman, nulliparous, with no history of previous abdominal surgeries or known pelvic enedometriosis, who consulted in January 2013 for pain in the abdominal wall and umbilical bleeding, coinciding with her last three menstruations. The physical examination reveals a deep retroumbilical induration that is tender on palpation. The ultrasound of the umbilical region reported: three supraponeurotic nodules, the largest 1 cm in diameter, with clear borders, with posterior acoustic shadow. Inside, mixed image with septa and and finely echogenic (bloody content?), with increased vascularization on Doppler examination. The gynecological ultrasound reported normal internal genitalia, with no signs of endometriosis. Two differential diagnoses arose: cutaneous inclusion cysts or primary umbilical endometriosis. Surgical resection is performed in February 2013. Microscopic examination confirmed the diagnosis of primary umbilical endometriosis. The patient had a daughter by cesarean section in 2016. During the procedure the pelvic cavity was examined and was completely free from of endometriosis. Extra-pelvic primary endometriosis is exceptional. The ectopic endometrial tissue response to hormonal stimulation explains the pain and the bleeding in the umbilical area, coinciding with menstrual periods. Clinical findings and imaging studies supported the presumptive diagnosis. The patient was successfully treated with surgery. The histopathology confirmed the diagnosis. The patient outcome was satisfactory.
publisher Universidad Nacional Córdoba. Facultad de Ciencias Médicas. Secretaria de Ciencia y Tecnología
publishDate 2021
url https://revistas.unc.edu.ar/index.php/med/article/view/34898
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first_indexed 2024-09-03T21:02:43Z
last_indexed 2024-09-03T21:02:43Z
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spelling I10-R327-article-348982024-04-15T16:19:09Z Primary endometriosis of umbilical location Endometriosis primaria de localización umbilical A Franco , GF Medina, A Briancon Ayo , M Moya , M Kasparian , A surgery Endometriosis clasificacation diagnosis clasificación diagnóstico cirugía Endometriosis . Abstract:  Endometriosis is defined as the presence of functioning endometrial tissue outside the uterine cavity, usually within the pelvis. Exceptionally, secondary extrapelvic involvement is seen involving the skin, related to scars from previous surgeries in patients with a proven pelvic endometriosis. Primary extrapelvic endometriosis (without pelvic involvement) is exceptional and its prevalence is unknown. There are just a few case reports of perianal, inguinal or other regions involvement. The age of presentation of extrapelvic cases ranges between 30 and 40 years, in contrast to cases with pelvic involvement, between 25 and 30 years. We present a 35-year-old woman, nulliparous, with no history of previous abdominal surgeries or known pelvic enedometriosis, who consulted in January 2013 for pain in the abdominal wall and umbilical bleeding, coinciding with her last three menstruations. The physical examination reveals a deep retroumbilical induration that is tender on palpation. The ultrasound of the umbilical region reported: three supraponeurotic nodules, the largest 1 cm in diameter, with clear borders, with posterior acoustic shadow. Inside, mixed image with septa and and finely echogenic (bloody content?), with increased vascularization on Doppler examination. The gynecological ultrasound reported normal internal genitalia, with no signs of endometriosis. Two differential diagnoses arose: cutaneous inclusion cysts or primary umbilical endometriosis. Surgical resection is performed in February 2013. Microscopic examination confirmed the diagnosis of primary umbilical endometriosis. The patient had a daughter by cesarean section in 2016. During the procedure the pelvic cavity was examined and was completely free from of endometriosis. Extra-pelvic primary endometriosis is exceptional. The ectopic endometrial tissue response to hormonal stimulation explains the pain and the bleeding in the umbilical area, coinciding with menstrual periods. Clinical findings and imaging studies supported the presumptive diagnosis. The patient was successfully treated with surgery. The histopathology confirmed the diagnosis. The patient outcome was satisfactory. Resumen:  La endometriosis se define como la presencia de tejido endometrial funcionante fuera de la cavidad uterina. Su localización típica es en pelvis. Excepcionalmente se presenta afectación extrapelvica (secundaria), generalmente cutánea, asociada a cicatrices de cirugías previas en pacientes con endometriosis pélvica constatada. Las formas extrapelvianas primarias, es decir sin compromiso pélvico, son excepcionales y se desconoce su prevalencia. Solo hay reportes de casos aislados con afectación en región perianal, inguinal u otras . La edad de presentación de los casos extrapélvicos oscila entre los 30 y 40 años, en contraste con los casos con compromiso pelviano, que se observan entre los 25 y 30 años. Presentamos el caso de una mujer de 35 años de edad, nulipara, sin antecedentes de cirugias previas ni de enedometriosis pélvica, que consulta en enero del año 2013 por dolor en la pared abdominal y hemorragia umbilical coincidente con sus tres últimas menstruaciones. El examen físico objetiva una induracion retroumbilical profunda que es dolorosa a la palpación.  Se solicitó una ecografía de la región umbilical que informa: tres nódulos supraponeuroticos, el mayor de 1 cm de diámetro, de bordes netos, con sombra acustica posterior. En su interior, imagen mixta con septos y y finamente ecogénica (contenido sanguinolento?), con aumento de la vascularizacion al examen Doppler. La ecografía ginecológica informó genitales internos normales, sin signos de endometriosis. Se plantean como diagnósticos diferenciales: quistes de inclusión cutáneos o focos de endometriosis. Se indica la resección quirúrgica en febrero del 2013. El examen microscópico confirmó el diagnóstico de endometriosis umbilical primaria. La paciente tuvo una hija por cesárea en el año 2016. Durante el procedimiento se examinó la cavidad pelviana, no pudiendo objetivar focos de endometriosis. la endometriosis primaria extra pélvica se presenta excepcionalmente. La respuesta a la estimulación hormonal del tejido endometrial ectópico explican el dolor y sangrado de la zona umbilical, en coincidencia con los períodos menstruales. Las manifestaciones clínicas y los estudios de imágenes apoyaron el diagnóstico presuntivo. La paciente fue tratada con cirugía. El estudio histopatológico confirmó el diagnóstico. La evolución de la paciente fue satisfactoria.  . Universidad Nacional Córdoba. Facultad de Ciencias Médicas. Secretaria de Ciencia y Tecnología 2021-10-12 info:eu-repo/semantics/article info:eu-repo/semantics/publishedVersion texto texto texto https://revistas.unc.edu.ar/index.php/med/article/view/34898 Revista de la Facultad de Ciencias Médicas de Córdoba.; Vol. 78 No. Suplemento (2021): Suplemento JIC XXII Revista de la Facultad de Ciencias Médicas de Córdoba; Vol. 78 Núm. Suplemento (2021): Suplemento JIC XXII Revista da Faculdade de Ciências Médicas de Córdoba; v. 78 n. Suplemento (2021): Suplemento JIC XXII 1853-0605 0014-6722 http://creativecommons.org/licenses/by-nc/4.0